Blood spots on Guthrie cards can be used for inherited tetrahydrobiopterin deficiency screening in hyperphenylalaninaemic infants.

نویسندگان

  • R J Leeming
  • P A Barford
  • J A Blair
  • I Smith
چکیده

We describe a method of screening for dihydropteridine reductase deficiency and dihydrobiopterin synthesis deficiency--the two inherited defects that cause tetrahydrobiopterin deficiency--using blood spots on Guthrie cards. Dihydropteridine reductase deficiency may be identified positively, and a biopterin value of less than 6.0 micrograms/l in the presence of hyperphenylalaninaemia indicates further investigation for dihydrobiopterin synthesis deficiency.

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عنوان ژورنال:
  • Archives of disease in childhood

دوره 59 1  شماره 

صفحات  -

تاریخ انتشار 1984